Wilson's disease or hepatolenticular degeneration is an autosomal recessive genetic disorder in which copper accumulates in tissues; this manifests as neurological or psychiatric symptoms and liver disease.
(wiki cakap..huhu)
Treatment
Treatment for Wilson's disease is effective if diagnosis occurs before the onset of life-threatening symptoms. The goal of treatment is to remove excessive copper from the body and prevent it from reaccumulating. If treatment is stopped, the disease can be fatal.
1. Drug Treatment
a. Penicillamine (Cuprimine, Depen)
b. Trientine (Syprine)
c. Zinc acetate (Galzin)
2. Dietary Therapy
a. Dietary changes require avoiding certain foods yang ni aq suka nak xplain ckit, namenye penyakit hati n kene elakkan makan hati jugak.. cam klaka lak.. hee.. seyes ni jangan makan hati sebab high copper lam hati.. coklat, kacang and cendawan pun kene elak.. xlbey dp skali sminggu.. xdea xmkan langsung.. ok ^^
b. Vitamin E supplements
c. A low-copper diet
3. Liver Transplantation
Expectations (prognosis)
Lifelong treatment is required to control the disorder. The disorder may cause fatal effects, especially loss of liver function and toxic effects of copper on the nervous system. In cases where the disorder is not fatal, symptoms may be disabling.